Erythromelalgia of the Ears: An Unusual Variant and Response to Therapy
March 2008 | Volume 7 | Issue 3 | Case Reports | 285 | Copyright © March 2008
David R. Berk MD, Arthur Z. Eisen MD
Erythromelalgia is characterized by episodes of erythematous, warm, burning acral skin, which is exacerbated by heat and
relieved by cold. Erythromelalgia usually affects the feet and/or hands but, although rare, erythromelalgia may affect the
ears. The authors present a 65-year-old woman with erythromelalgia of the ears with disabling symptoms whose diagnosis
was delayed for 6 years. The patient failed to respond to numerous therapies before rapidly improving with oral amitriptyline
and amitriptyline 1% to 2% and ketamine 0.5% to 1% topical gel.